pediatric dentistry and dental public health department, Faculty of dentistry, Alexandria university, Alexandria ,Egypt
Abstract
Abstract: Ectodermal dysplasia (ED) is an uncommon genetic disorder that results from abnormalities in the development of tissues, organs, and other structures that originate from the embryonic ectoderm. This condition is rare, occurring in approximately 1 out of every 100,000 births. In this condition anodontia or hypodontia may be associated with other ectodermal abnormalities, such as anhidrosis, hypotrichosis, asteatosis, and defects in salivary glands.The clinical manifestations of ED lead to a significant social challenges for those affected. Here, we present one such case of ectodermal dysplasia in 13-year-old patient, in which removable partial dentures was inserted for oral rehabilitation. Providing a comprehensive medical care to patients with ED requires a multidisciplinary approach, involving a team that includes pediatricians or physicians as well as a prosthodontist, pedodontist, and orthodontist. Additionally, consultations with a child psychologist and dermatologist should be considered Keywords: Hypodontia, Hypohidrosis, Hypohydrotic ectodermal dysplasia (HED), Partial anodontia, multidisciplinary approach, case report.
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